Progressive Hemifacial Atrophy With Contralateral Uveitis: A Case Report

نویسندگان

  • Onder Ayyildiz
  • Simel Ayyildiz
  • Ali Hakan Durukan
  • Gungor Sobaci
چکیده

INTRODUCTION Progressive hemifacial atrophy, known as Parry-Romberg syndrome (PRS), was first described by Parry in 1825. There is a progressive atrophy of facial tissues including skin, bones and muscles. Ophthalmic disorders are common and include keratitis, uveitis, cataract, ipsilateral enophthalmos, optic neuritis, retinal vasculitis and scleral melting. CASE PRESENTATION We describe a patient with progressive hemifacial atrophy at right facial side who developed granulomatous uveitis and periferic retinal vasculitis in his left eye. We started topical and systemic steroid therapy. Uveitic reaction had regressed almost entirely after a 3-month steroid treatment. CONCLUSIONS The individuals should have multidisciplinary approach for the variety of disorders to maintain the appropriate treatment for a better appearance of the patients.

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عنوان ژورنال:

دوره 17  شماره 

صفحات  -

تاریخ انتشار 2015